Cherubism: early surgical approach and its effects on the quality of life in a pediatric patient

Laryssa Thainá Mello Queiroz Cunha; Almira Oliveira Pereira; Roniery Correia Santos; Eduardo Zancopé; Sebastião  Alves Pinto; Valtuir Barbosa Félix; Rubens Jorge Silveira

doi:10.5327/2525-5711.326

Autores

Laryssa Thainá Mello Queiroz Cunha State University of Campinas, Piracicaba Dental School, Department of oral diagnosis – Piracicaba (SP), Brazil. https://orcid.org/0000-0003-1357-4129
Almira Oliveira Pereira State University of Campinas, Piracicaba Dental School, Department of oral diagnosis – Piracicaba (SP), Brazil. https://orcid.org/0000-0003-0888-8449
Roniery Correia Santos Instituto de Pós-Graduação e Graduação, Department of Psychology – Goiânia (GO), Brazil. https://orcid.org/0000-0002-8481-1147
Eduardo Zancopé Federal University of Uberlândia, School of Dentistry, Department of Occlusion – Uberlândia (MG), Brazil. https://orcid.org/0000-0002-6567-4810
Sebastião Alves Pinto Goiano Institute of Oncology and Hematology – Goiânia (GO), Brazil. https://orcid.org/0000-0001-6887-5231
Valtuir Barbosa Félix Federal University of Alagoas, University Hospital, Department of Oral Pathology – Maceió (AL), Brazil. https://orcid.org/0000-0002-2961-2487
Rubens Jorge Silveira Pontifical Catholic University of Goiás, Department of Oral and Maxillofacial Surgery and Traumatology – Goiânia (GO), Brazil. https://orcid.org/0000-0002-3234-2158

DOI:

https://doi.org/10.5327/2525-5711.326

Palavras-chave:

Cherubism, Facial deformities, Quality of life

Resumo

Querubismo é uma osteodisplasia fibro-óssea rara caracterizada pela expansão simétrica dos maxilares, frequentemente levando a deformidades faciais e comprometimento funcional. Este estudo apresenta o caso de um paciente pediátrico diagnosticado com querubismo que foi submetido a intervenção cirúrgica precoce para melhorar a qualidade de vida e reduzir os impactos psicossociais associados à doença. O questionário PedsQL™ 4.0 foi aplicado para avaliar a qualidade de vida antes e depois do procedimento cirúrgico. Os resultados demonstraram uma melhora significativa nos domínios social e escolar, refletindo uma redução na carga psicossocial do querubismo. Seis meses após o procedimento, nenhuma complicação significativa ou sinais de recorrência foram observados, destacando a eficácia da intervenção precoce. Esses achados sugerem que uma abordagem cirúrgica precoce é uma estratégia valiosa para otimizar a qualidade de vida e minimizar os efeitos negativos do querubismo, particularmente em crianças em desenvolvimento social e acadêmico.

Palavras-chave: Querubismo; Deformidades faciais; Qualidade de vida.

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